Cannabidiol (8) – Epidyolex®

Seizures associated with tuberous sclerosis, ≥ 2 years

Characteristics

Start date 01.12.2023 – Marketing authorisation: 16.04.2021
Resolution 16.05.2024
INN Cannabidiol
Brand name Epidyolex®
Pharm. company Dossier: Jazz Pharmaceuticals Germany GmbH
New distributor: JAZZ PHARMACEUTICALS IRELAND LIMITED
G-BA Procedure ID D-1017
ATC code N03AX24 Other antiepileptics (N03AX)
ICD-10 codes (AIS) Q85.1Bourneville´s disease
Alpha-ID codes (AIS) I16625Tuberous sclerosis
ORPHAcodes (AIS) 805Tuberous sclerosis
Therapeutic area Other diseases Epilepsy, Seizures Orphan (turnover limit)
Reason for procedure Reassessment: Orphan turnover exceeded
Original resolution: Cannabidiol (5) (04.11.2021)
Specialty Bundling ACT change Combination therapy

Therapeutic indication of the resolution

Epidyolex is used as an add-on therapy for seizures associated with tuberous sclerosis (TSC) in patients aged 2 years and older.

Subpopulation Indication Comparator
Patients aged 2 years and older with seizures associated with tuberous sclerosis Patient-specific therapy, taking into account the type of seizure occurring, the basic and previous therapy(s) and any associated side effects, with selection of brivaracetam, carbamazepine, cenobamate, eslicarbazepine, everolimus, gabapentin, lacosamide, lamotrigine, levetiracetam, oxcarbazepine, perampanel, phenobarbital, phenytoin, pregabalin, topiramate, valproic acid, vigabatrin, zonisamide

Studies and Results

No. of studies
(best subpopulation)
0 (Data not accepted)
Study design
(best subpopulation)
Data not accepted (Dossier: H2H vs. non-ACT + no ITC)
ACT change 03.04.2024 – Stellungnahme Fachgesellschaften

  • Clinical trials
    • This was a randomised, controlled, double-blind trial in which cannabidiol was compared with placebo, in each case in addition to ongoing anti-epileptic treatment.

Patients aged 2 years and over with seizures associated with tuberous sclerosis

  • For patients aged 2 years and over with seizures associated with tuberous sclerosis, the additional benefit is not proven.
  • The additional benefit of cannabidiol compared with the appropriate comparator therapy for patients aged 2 years and over with seizures associated with tuberous sclerosis is not proven.
  • In the study relevant to this benefit assessment, no optimisation of antiepileptic treatment was planned for patients in the comparator arm.
  • Although the included patients experienced regular epileptic seizures, the existing anti-epileptic medication in the comparator arm was supplemented only with placebo and was therefore continued unchanged.
  • The appropriate comparator therapy was therefore not implemented in the study submitted for the benefit assessment.
  • Overall review
    • Overall, there are no suitable data available for comparing cannabidiol with the appropriate comparator therapy.

Courtesy translation only, please refer to the German original.

Associated procedures

Cannabidiol (6) Epidyolex® Jazz Pharmaceuticals Germany GmbH Nervous system diseases Dravet syndrome, ≥ 2 years, combination with clobazam 0
500–2,900
100% additional benefit not proven Orphan (turnover limit) repealed
Cannabidiol (7) Epidyolex® Jazz Pharmaceuticals Germany GmbH Nervous system diseases Lennox-Gastaut syndrome, ≥ 2 years, combination with clobazam 1,700–22,700 100% additional benefit not proven Orphan (turnover limit)
Cannabidiol (8) Epidyolex® Jazz Pharmaceuticals Germany GmbH Other diseases Seizures associated with tuberous sclerosis, ≥ 2 years 200–2,700 100% additional benefit not proven Orphan (turnover limit)
Cannabidiol (5) Epidyolex® GW Pharmaceuticals plc Other diseases Seizures in Tuberous Sclerosis, ≥ 2 years 0
500–2,700
100% Hint for non-quantifiable additional benefit Orphan repealed
Cannabidiol (4) Epidyolex® GW Pharmaceuticals plc Nervous system diseases Lennox-Gastaut syndrome, ≥ 2 years, combination with clobazam 0
2,600–22,700
100% Hint for considerable additional benefit Orphan repealed
Cannabidiol (3) Epidyolex® GW Pharmaceuticals plc Nervous system diseases Dravet syndrome, ≥ 2 years, combination with clobazam 0
1,100–3,100
100% Hint for considerable additional benefit Orphan repealed
Cannabidiol (1) Epidyolex® GW Pharmaceuticals plc Nervous system diseases Dravet syndrome, ≥ 2 years, combination with clobazam 0
1,100–3,100
100% Hint for non-quantifiable additional benefit Orphan repealed
Cannabidiol (2) Epidyolex® GW Pharmaceuticals plc Nervous system diseases Lennox-Gastaut syndrome, ≥ 2 years, combination with clobazam 0
2,600–22,700
100% Hint for non-quantifiable additional benefit Orphan repealed


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