Cannabidiol (6) – Epidyolex®

Dravet syndrome, ≥ 2 years, combination with clobazam

Characteristics

Start date 01.12.2023 – Marketing authorisation: 19.09.2019
Resolution 16.05.2024 repealed
INN Cannabidiol
Brand name Epidyolex®
Pharm. company Dossier: Jazz Pharmaceuticals Germany GmbH
New distributor: JAZZ PHARMACEUTICALS IRELAND LIMITED
G-BA Procedure ID D-1015
ATC code N03AX24 Other antiepileptics (N03AX)
ICD-10 codes (AIS) G40.4Epilepsy with grand mal seizures on awakening
Alpha-ID codes (AIS) I128083Dravet syndrome
ORPHAcodes (AIS) 33069Dravet syndrome
Therapeutic area Nervous system diseases Epilepsy, Epilepsy in children (Dravet syndrome / Lennox-Gastaut syndrome) Orphan (turnover limit)
Reason for procedure Reassessment: Orphan turnover exceeded
Original resolution: Cannabidiol (3) (15.04.2021)
Specialty Bundling ACT change Combination therapy

Therapeutic indication of the resolution

Epidyolex is used as adjunctive therapy for seizures associated with Lennox-Gastaut syndrome (LGS) or Dravet syndrome (DS) in combination with clobazam in patients aged 2 years and older.

Subpopulation Indication Comparator
Patients aged 2 years and older with seizures associated with Dravet syndrome Patient-specific therapy, taking into account the type of seizure occurring, the basic therapy and previous therapy(s) as well as any associated side effects, selecting brivaracetam, bromide, clobazam, fenfluramine, levetiracetam, stiripentol, topiramate, valproic acid

Studies and Results

No. of studies
(best subpopulation)
0 (Data not accepted)
Study design
(best subpopulation)
Data not accepted (Dossier: H2H vs. non-ACT + no ITC)
ACT change 03.04.2024 – Stellungnahme der Fachgesellschaften

  • Clinical trials
    • These were two randomised, controlled, double-blind trials in which cannabidiol was compared with placebo, in each case in addition to ongoing anti-epileptic treatment.

Patients aged 2 years and over with seizures associated with Dravet syndrome

  • For patients aged 2 years and over with seizures associated with Dravet syndrome, the additional benefit is not proven.
  • The additional benefit of cannabidiol compared with the appropriate comparator therapy for patients aged 2 years and over with seizures associated with Dravet syndrome is therefore not proven.
  • Overall assessment
    • In the overall review, there are no suitable data available for comparing cannabidiol with the appropriate comparator therapy. Consequently, the additional benefit of cannabidiol for patients aged 2 years and over with seizures associated with Dravet syndrome is not proven.

Courtesy translation only, please refer to the German original.

Associated procedures

Cannabidiol (6) Epidyolex® Jazz Pharmaceuticals Germany GmbH Nervous system diseases Dravet syndrome, ≥ 2 years, combination with clobazam 0
500–2,900
100% additional benefit not proven Orphan (turnover limit) repealed
Cannabidiol (7) Epidyolex® Jazz Pharmaceuticals Germany GmbH Nervous system diseases Lennox-Gastaut syndrome, ≥ 2 years, combination with clobazam 1,700–22,700 100% additional benefit not proven Orphan (turnover limit)
Cannabidiol (8) Epidyolex® Jazz Pharmaceuticals Germany GmbH Other diseases Seizures associated with tuberous sclerosis, ≥ 2 years 200–2,700 100% additional benefit not proven Orphan (turnover limit)
Cannabidiol (5) Epidyolex® GW Pharmaceuticals plc Other diseases Seizures in Tuberous Sclerosis, ≥ 2 years 0
500–2,700
100% Hint for non-quantifiable additional benefit Orphan repealed
Cannabidiol (4) Epidyolex® GW Pharmaceuticals plc Nervous system diseases Lennox-Gastaut syndrome, ≥ 2 years, combination with clobazam 0
2,600–22,700
100% Hint for considerable additional benefit Orphan repealed
Cannabidiol (3) Epidyolex® GW Pharmaceuticals plc Nervous system diseases Dravet syndrome, ≥ 2 years, combination with clobazam 0
1,100–3,100
100% Hint for considerable additional benefit Orphan repealed
Cannabidiol (1) Epidyolex® GW Pharmaceuticals plc Nervous system diseases Dravet syndrome, ≥ 2 years, combination with clobazam 0
1,100–3,100
100% Hint for non-quantifiable additional benefit Orphan repealed
Cannabidiol (2) Epidyolex® GW Pharmaceuticals plc Nervous system diseases Lennox-Gastaut syndrome, ≥ 2 years, combination with clobazam 0
2,600–22,700
100% Hint for non-quantifiable additional benefit Orphan repealed


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