Tafamidis (3) – Vyndaqel®

Amyloid Neuropathy

Characteristics

Start date 01.12.2020 – Marketing authorisation: 16.11.2011
Resolution 20.05.2021
INN Tafamidis
Brand name Vyndaqel®
Pharm. company Pfizer Pharma GmbH
G-BA Procedure ID D-611
ATC code N07XX08 Other nervous system drugs (N07XX)
ICD-10 codes (AIS) E85.0Non-neuropathic heredofamilial amyloidosis, E85.1Amyloid polyneuropathy (Portuguese), E85.2Heredofamilial amyloidosis, unspecified, E85.4Localized amyloidosis, E85.8Other amyloidosis, E85.9Amyloidosis, unspecified
Alpha-ID codes (AIS) I129348Hereditary transthyretin amyloidosis, I129352Wild-type transthyretin amyloidosis, I24316Amyloidosis, I2490Non-neuropathic heredofamilial amyloidosis, I2491Neuropathic heredofamilial amyloidosis, I66392Localized amyloidosis
ORPHAcodes (AIS) 271861Hereditary transthyretin amyloidosis, 330001Wild-type transthyretin amyloidosis, 69Amyloidosis,
DDD 20 mg O
Therapeutic area Metabolic diseases Amyloidosis Orphan (turnover limit)
Reason for procedure Reassessment: Orphan turnover exceeded
Original resolution: Tafamidis (1) (07.06.2012)
Regulatory status Exceptional Circumstances
Specialty Bundling

Therapeutic indication of the resolution

Vyndaqel is indicated for the treatment of transthyretin amyloidosis in adult patients with stage 1 symptomatic polyneuropathy to delay peripheral neurologic impairment.

Subpopulation Indication Comparator
Adult patients with transthyretin amyloidosis with symptomatic stage 1 polyneuropathy Patisiran

Studies and Results

No. of studies
(best subpopulation)
0 (no data submitted)
Study design
(best subpopulation)
no data submitted

  • Clinical trials
    • In its dossier for the assessment of the additional benefit of Tafamidis, the pharmaceutical manufacturer does not present any direct comparative studies against the appropriate comparator therapy.
    • Furthermore, no indirect comparisons were presented to address the issues raised in the benefit assessment.

Adult patients with transthyretin amyloidosis and symptomatic stage 1 polyneuropathy

  • For adult patients with transthyretin amyloidosis and symptomatic stage 1 polyneuropathy, the additional benefit of Tafamidis compared with the appropriate comparator therapy is not proven.
  • In its dossier for the assessment of the additional benefit of tafamidis, the pharmaceutical manufacturer does not present any direct comparative studies against the appropriate comparator therapy.
  • Furthermore, no indirect comparisons were submitted to address the issues raised in the benefit assessment.
  • Consequently, there are no suitable data available overall for the assessment of the additional benefit of Tafamidis.
  • Overall assessment
    • On balance, for adult patients with transthyretin amyloidosis and symptomatic stage 1 polyneuropathy, the additional benefit of Tafamidis compared with the appropriate comparator therapy is not proven.

Courtesy translation only, please refer to the German original.

Associated procedures

Tafamidis (4) Vyndaqel® Pfizer Pharma GmbH Metabolic diseases Amyloid cardiomyopathy 1,760–1,810 100% Indication of considerable additional benefit Orphan (turnover limit)
Tafamidis (3) Vyndaqel® Pfizer Pharma GmbH Metabolic diseases Amyloid Neuropathy 230 100% additional benefit not proven Orphan (turnover limit)
Tafamidis (2) Vyndaqel® Pfizer Pharma GmbH Metabolic diseases Amyloid cardiomyopathy 0
1,630–1,730
100% Hint for considerable additional benefit Orphan repealed
Tafamidis (1) Vyndaqel® Pfizer Pharma GmbH Metabolic diseases Amyloid Neuropathy 0
40–104
100% minor additional benefit Orphan repealed


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