Nintedanib (Ofev, 6) – Ofev®

Interstitial lung disease with systemic sclerosis, 6 to < 18 years of age

Characteristics

Start date 15.02.2025 – Marketing authorisation: 12.02.2025
Resolution 07.08.2025
INN Nintedanib
Brand name Ofev®
Pharm. company Boehringer Ingelheim Pharma GmbH
G-BA Procedure ID D-1157
ATC code L01EX09 Other protein kinase inhibitors (L01EX)
ICD-10 codes (AIS) J84.90, M34.8Other forms of systemic sclerosis
Alpha-ID codes (AIS) I111403Interstitial lung disease
Therapeutic area Respiratory system diseases Interstitial lung disease (ILD)
Reason for procedure New therapeutic indication
Specialty Bundling Patent/data protection expired

Therapeutic indication of the resolution

Ofev is used for the treatment of interstitial lung disease in children and adolescents aged 6 to 17 years with systemic sclerosis (SSc-ILD).

Subpopulation Indication Comparator
Children and adolescents aged 6 to 17 years with interstitial lung disease with systemic sclerosis (SSc-ILD) Best Supportive Care

Studies and Results

No. of studies
(best subpopulation)
1 (InPedILD) 0 (Data not accepted)
Study design
(best subpopulation)
Data not accepted (Dossier: H2H vs. non-ACT + no ITC)

  • Clinical trials
    • In the dossier for the benefit assessment, the pharmaceutical manufacturer submitted the results of the InPedILD study. This was a randomised, double-blind, parallel-group study comparing nintedanib with placebo, both administered in addition to standard therapy at the discretion of the doctor.

Children and adolescents aged 6 to 17 years with interstitial lung disease associated with systemic sclerosis (SSc-ILD)

  • An additional benefit is not proven for children and adolescents aged 6 to 17 years with interstitial lung disease associated with systemic sclerosis (SSc-ILD).
  • An additional benefit of nintedanib is not proven.
  • The pharmaceutical manufacturer states that the InPedILD study included only 7 children and adolescents with interstitial lung disease associated with systemic sclerosis and that, due to the small number of children and adolescents, no conclusions can be drawn for the assessment of additional benefit.
  • Consequently, the pharmaceutical manufacturer did not prepare any data for the dossier relating to this specific question.
  • Consequently, there are no suitable data available to assess the additional benefit of nintedanib for children and adolescents aged 6 to 17 years with interstitial lung disease associated with systemic sclerosis.

Courtesy translation only, please refer to the German original.

Associated procedures

Nintedanib (Ofev, 6) Ofev® Boehringer Ingelheim Pharma GmbH Respiratory system diseases Interstitial lung disease with systemic sclerosis, 6 to < 18 years of age 0–8 100% additional benefit not proven
Nintedanib (Ofev, 5) Ofev® Boehringer Ingelheim Pharma GmbH Respiratory system diseases Clinically significant progressive fibrosing interstitial lung disease, 6 to < 18 years of age 1–35 100% additional benefit not proven
Nintedanib (Ofev, 3) Ofev® Boehringer Ingelheim Pharma GmbH & Co. KG Respiratory system diseases Interstitial pulmonary disease with systemic sclerosis 200–10,700 100% additional benefit not proven
Nintedanib (Ofev, 4) Ofev® Boehringer Ingelheim Pharma GmbH & Co. KG Respiratory system diseases Progressive fibrosing interstitial lung diseases 4,500–11,400 100% Indication of minor additional benefit
Nintedanib (Ofev, 2) Ofev® Boehringer Ingelheim Pharma GmbH & Co. KG Respiratory system diseases Idiopathic pulmonary fibrosis 1,800–18,900 100% Hint for considerable additional benefit Orphan (turnover limit)
Nintedanib (Ofev, 1) Ofev® Boehringer Ingelheim Pharma GmbH & Co KG Respiratory system diseases Idiopathic pulmonary fibrosis 0
2,080–19,700
100% minor additional benefit Orphan repealed


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