Burosumab (6) – Crysvita®

FGF23-related hypophosphatemia in tumour-induced osteomalacia

Characteristics

Start date 01.09.2022 – Marketing authorisation: 25.07.2022
Resolution 16.02.2023
INN Burosumab
Brand name Crysvita®
Pharm. company Kyowa Kirin GmbH
G-BA Procedure ID D-852
ATC code M05BX05 Other drugs affecting bone structure and mineralization (M05BX)
ICD-10 codes (AIS) E83.38, M83.89
Alpha-ID codes (AIS) I128133Oncogenic osteomalacia, I65880Acquired hypophosphatemia
ORPHAcodes (AIS) 352540Oncogenic osteomalacia,
DDD 2.5 mg P
Therapeutic area Metabolic diseases Hypophosphatemia Orphan (turnover limit)
Reason for procedure New therapeutic indication – Orphan turnover exceeded

Therapeutic indication of the resolution

Crysvita is used for the treatment of FGF23-related hypophosphatemia in tumour-induced osteomalacia associated with phosphaturic mesenchymal tumors that cannot be curatively treated by surgery or cannot be localised, in children and adolescents aged 1 to 17 years, and in adults.

Subpopulation Indication Comparator
Patients 1 year and older with FGF23-related hypophosphatemia in tumour-induced osteomalacia associated with phosphaturic mesenchymal tumours that cannot be curatively treated by surgery or cannot be localised. A phosphate substitution and active vitamin D (calcitriol or alfacalcidol) in combination

Studies and Results

No. of studies
(best subpopulation)
0 (no data submitted)
Study design
(best subpopulation)
no data submitted (Dossier: Single-arm + no comparison)

  • Clinical trials
    • To assess the additional benefit of buurosumab for patients aged 1 year and over with FGF23-related hypophosphataemia in tumour-induced osteomalacia (TIO), associated with phosphaturic mesenchymal tumours that cannot be curatively treated by surgery or cannot be localised, the pharmaceutical manufacturer submitted the two open-label, single-arm Phase II studies UX023T-CL201 and KRN23-002, which formed the basis for the marketing authorisation.
    • The single-arm study UX023T-CL201 included adult patients with TIO as well as patients with osteomalacia associated with epidermal naevus syndrome (ENS).
    • A total of 14 adult patients with TIO were enrolled in the single-arm study KRN23-002.

Patients aged 1 year and over with FGF23-related hypophosphataemia in tumour-induced osteomalacia, associated with phosphaturic mesenchymal tumours that cannot be curatively treated by surgery or cannot be localised

  • The additional benefit is not proven.
  • An additional benefit of burosumab compared with the appropriate comparator therapy is not proven.
  • Burosumab may represent a relevant treatment option in individual cases within the present therapeutic indication.
  • Overall, the pharmaceutical manufacturer did not submit any study for this therapeutic indication that would have been suitable for assessing the additional benefit of Burosumab compared with the appropriate comparator therapy.

Courtesy translation only, please refer to the German original.

Associated procedures

Burosumab (7) Crysvita® Kyowa Kirin GmbH Metabolic diseases X-linked hypophosphataemia; ≥ 1 month to < 1 year n.d. active procedure Orphan (turnover limit)
Burosumab (6) Crysvita® Kyowa Kirin GmbH Metabolic diseases FGF23-related hypophosphatemia in tumour-induced osteomalacia 60–140 100% additional benefit not proven Orphan (turnover limit)
Burosumab (5) Crysvita® Kyowa Kirin GmbH Metabolic diseases X-linked hypophosphatemia, ≥ 18 years of age 410–810 100% additional benefit not proven Orphan (turnover limit)
Burosumab (4) Crysvita® Kyowa Kirin GmbH Metabolic diseases X-linked hypophosphatemia, ≥ 1 to < 18 years of age 200–550 100% Hint for non-quantifiable additional benefit Orphan (turnover limit)
Burosumab (3) Crysvita® Kyowa Kirin GmbH Metabolic diseases X-linked hypophosphatemia (XLH), ≥ 18 years 0
410–810
100% Hint for minor additional benefit Orphan repealed
Burosumab (2) Crysvita® Kyowa Kirin GmbH Metabolic diseases X-linked hypophosphatemia (XLH), ≥ 1 to < 18 years 0
200–500
100% Hint for non-quantifiable additional benefit Orphan repealed
Burosumab (1) Crysvita® Kyowa Kirin GmbH Metabolic diseases X-linked hypophosphatemia (XLH), ≥ 1 to < 18 years 0
200–500
100% non-quantifiable additional benefit Orphan repealed


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