Avapritinib (6) – Ayvakyt®

Gastrointestinal stromal tumours

Characteristics

Start date 01.11.2025 – Marketing authorisation: 24.09.2020
Resolution 16.04.2026
INN Avapritinib
Brand name Ayvakyt®
Pharm. company Blueprint Medicines (Germany) GmbH
G-BA Procedure ID D-1263
ATC code L01EX18 Other protein kinase inhibitors (L01EX)
ICD-10 codes (AIS) C15.9Malignant neoplasm of esophagus, unspecified, C16.9Gastric cancer NOS, C17.9Malignant neoplasm of small intestine, unspecified, C18.9Malignant neoplasm of large intestine NOS, C26.9Malignant neoplasm of ill-defined sites within the digestive system, C48.2Malignant neoplasm of peritoneum, unspecified
Alpha-ID codes (AIS) I117054Gastrointestinal stromal tumor, I134833GIST (gastrointestinal stromal tumor) of the small intestine, I134850GIST (gastrointestinal stromal tumor) of the esophagus, I134868GIST (gastrointestinal stromal tumor) of the stomach, I134898GIST (gastrointestinal stromal tumor) of the colon, I134908GIST (gastrointestinal stromal tumor) of the peritoneum
ORPHAcodes (AIS) 44890Gastrointestinal stromal tumor, 44890GIST (gastrointestinal stromal tumor) of the small intestine, 44890GIST (gastrointestinal stromal tumor) of the esophagus, 44890GIST (gastrointestinal stromal tumor) of the stomach, 44890GIST (gastrointestinal stromal tumor) of the colon,
Therapeutic area Oncological diseases Orphan (turnover limit)
Reason for procedure Reassessment: Orphan turnover exceeded

Therapeutic indication of the resolution

Ayvakyt is indicated as monotherapy for the treatment of adult patients with inoperable or metastatic gastrointestinal stromal tumours (GIST) harbouring the platelet-derived growth factor receptor alpha (PDGFRA) PDGFRA) D842V mutation.

Subpopulation Indication Comparator
Erwachsene Patientinnen und Patienten mit inoperablen oder metastasierten gastrointestinalen Stromatumoren (GIST), die die Thrombozyten-Wachstumsfaktor-Rezeptoralpha (PDGFRA)-D842V-Mutation aufweisen

Studies and Results

  • Clinical trials
    • The NAVIGATOR study is a single-arm, multicentre Phase I study of avapritinib, divided into a dose-escalation phase (Part 1) and an expansion phase (Part 2).
    • The CS3007-101 trial is a non-randomised Phase I/II trial of avapritinib, conducted exclusively in China.

Adult patients with inoperable or metastatic gastrointestinal stromal tumours (GIST) harbouring the platelet-derived growth factor receptor alpha (PDGFRA) D842V mutation

  • The additional benefit is not proven.
  • Consequently, there are no suitable data available overall for assessing the additional benefit of avapritinib. Consequently, no additional benefit of avapritinib has been demonstrated for patients with inoperable or metastatic gastrointestinal stromal tumours (GIST) who carry the platelet-derived growth factor receptor alpha (PDGFRA)-D842V mutation, compared with the appropriate comparator therapy, does not provide proof.
  • mortality
    • The single-arm studies NAVIGATOR and CS3007-101 submitted by the pharmaceutical manufacturer do not allow for a comparison with the appropriate comparator therapy and are therefore not suitable for assessing the additional benefit of avapritinib as monotherapy.
  • morbidity
    • The single-arm studies NAVIGATOR and CS3007-101 submitted by the pharmaceutical manufacturer do not allow for a comparison with the appropriate comparator therapy and are therefore not suitable for assessing the additional benefit of avapritinib as monotherapy.
  • Side effects
    • The single-arm studies NAVIGATOR and CS3007-101 submitted by the pharmaceutical manufacturer do not allow for a comparison with the appropriate comparator therapy and are therefore not suitable for assessing the additional benefit of avapritinib as monotherapy.
  • Conclusion
    • The single-arm studies NAVIGATOR and CS3007-101 submitted by the pharmaceutical manufacturer do not allow for a comparison with the appropriate comparator therapy and are therefore not suitable for assessing the additional benefit of avapritinib as monotherapy.
    • The results of the VOYAGER study, which were already submitted in the dossier for the initial assessment and are presented comparatively in the results section, a propensity score (PS)-adjusted indirect comparison with the NAVIGATOR and BLU-285-1002 studies and the retrospective study by Cassier et al, 2012, were not analysed in the present procedure and are therefore not suitable for assessing additional benefit.
    • Consequently, there are no suitable data available overall for the assessment of the additional benefit of avapritinib.

Courtesy translation only, please refer to the German original.

Associated procedures

Avapritinib (4) Ayvakyt® Blueprint Medicines (Germany) GmbH Oncological diseases Indolent systemic mastocytosis (ISM) 715–1,000 100% Hint for minor additional benefit Orphan (turnover limit)
Avapritinib (6) Ayvakyt® Blueprint Medicines (Germany) GmbH Oncological diseases Gastrointestinal stromal tumours 5–60 100% additional benefit not proven Orphan (turnover limit)
Avapritinib (5) Ayvakyt® Blueprint Medicines (Germany) GmbH Oncological diseases Advanced systemic mastocytosis, following at least one prior course of treatment 260–680 100% additional benefit not proven Orphan (turnover limit)
Avapritinib (3) Ayvakyt® Blueprint Medicines GmbH Oncological diseases Indolent systemic mastocytosis (ISM) 0
715–1,000
100% Indication of minor additional benefit Orphan repealed
Avapritinib (2) Ayvakyt® Blueprint Medicines (Germany) GmbH Oncological diseases Systemic mastocytosis, after at least 1 prior therapy 0
270–680
100% Hint for non-quantifiable additional benefit Orphan repealed
Avapritinib (1) Ayvakyt® Blueprint Medicines (Germany) GmbH Oncological diseases Gastrointestinal stromal tumor (GIST) 0
1–90
100% Hint for non-quantifiable additional benefit Orphan repealed


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